Y-type urethral duplication: A case series of four cases with good outcome

Sarita Chowdhary, Shyamendra Pratap Sharma, Pranaya Kumar Panigrahi, Shiv Prasad Prasad Sharma

Abstract


Urethral duplication is a rare congenital condition. This case series intends to strengthen the concept of Y-type urethral duplication (new anatomic variation of an accessory limb of duplicated urethra). We have conducted a retrospective analysis collecting information from four cases of type IIA-2Y variety of urethral duplication (Effmann classification), which is one of rarely found subtype with its embryogenesis, diagnosis and single stage repair with outcome. Four babies  around 1- 6 months of age range (mean- 3.2  months), complaining  of  passing  urine  from  a  site  other  than  penis  which  includes anal canal, perineal area. All babies were investigated for other associated anomaly and were planned for surgery. Three out of four cases had undergone excision of accessory urethra and urethral stent in ventral urethra in postoperative period for 8-10 days with good results. In one case, posterior sagittal anorectoplasty (PSARP) approach was used to delineate accessory urethra and end to end urethral anastomosis was done with better outcome. All babies are on regular follow up till now ranging 6months to three years. It is important to delineate the functional urethra before planning for intervention so as to address the problem.


Keywords


Urethral duplication, Y-type urethra, orthotopic, heterotopic urethra

Full Text:

PDF

References


Effmann EL, Lebowitz RL, Colodny AH. Duplication of the urethra. Radiology. 1976; 119(1):179–185.

Lima M, Destro F, Di Salvo N, Gargano T, Ruggeri G. Fate of males with urethral "Y-duplication": 40-year long follow-up in 8 patients. J Pediatr Surg. 2017; 52(8):1335–39.

Okur MH, Aydogdu B, Arslan S, et al. Type II A2 duplication of urethra in an 8-month-old male child: A case report. Pediatr Urol Case Rep. 2015; 2(1):17-22.

Rintala RJ, Mildh L, Lindahl H. H-type anorectal malformations: incidence and clinical characteristics. J Pediatr Surg. 1996; 31(4):559–62.

Williams DI, Kenawi MM. Urethral duplications in the male. Eur Urol. 1975; 1(5):209–15.

Wagner JR, Carr MC, Bauer SB, et al. Congenital posterior urethral perineal fistulae: a unique form of urethral duplication. Urology. 1996; 48(2):277–80.

Mane SB, Obaidah A, Dhende NP, et al. Urethral duplication in children: our experience of eight cases. J Pediatr Urol. 2009; 5(5):363–67.

Ortolano V, Nasrallah PF. Urethral duplication. J Urol. 1986; 136(4):909–12.

Meier DE, Latiff A. Y-type congenital urethral duplication with normal dorsal urethra and small ventral fistula to perineal skin – 28th reported case. J Pediatr Surg Case Rep. 2016; 8:37–39.

Bello JO. Congenital posterior urethroperineal fistula: a review and report of the 25th case in literature. Urology. 2014; 84(6):1492–95.

Lopes RI, Giron AM, Mello MF, et al. Urethral duplication type influences on the complications rate and number of surgical procedures. Int Braz J Urol. 2017; 43(6):1144–51.

Tiwari C, Bothra J, Kumbhar V et al. A rare case of congenital Y-type urethral duplication. Pediatr Urol Case Rep. 2015; 2(6):20-26.

Raffoul L, Rod J, Ravasse P, Blanc T, Lortat-Jacob S. Q-island flap urethroplasty: 1-stage procedure for reconstruction of Y-type urethral duplications in children. J Urol. 2015; 193(6):2068–72.

Salle JL, Sibai H, Rosenstein D, Brzezinski AE, Corcos J. Urethral duplication in the male: review of 16 cases. J Urol. 2000; 163(6):1936–40.

Stephens FD, Donnellan WL. "H-type" urethroanal fistula. J Pediatr Surg. 1977; 12(1):95–102.




DOI: http://dx.doi.org/10.14534/j-pucr.2020359810

Refbacks

  • There are currently no refbacks.


Indexing/Abstracting

DOAJ, Tübitak/Ulakbim Turkish Medical Database, Academic OneFile, Health Reference Center Academic, US National Library of Medicine (NLM) Catalog, ICI Journals Master List (Index Copernicus), OCLC-WorldCat, Genamics-JournalSeek, J-Gate, Google Scholar, Ulrichsweb, CNKI Scholar, NAVER Academic, Research Bible, Cross Ref, EZB (Electronic Journals Library), JournalTOCs, HINARI, Norwegian Social Science Data Services (NSD), Turkiye Citation Index, SCIARY (Worldwide Science Educational Library), BASE (Bielefeld Academic Search Engine), NAIST, ICMJE, PubsHub, AcademicKeys, OAJI, OpenAIRE, Turk Medline, Publons, ROAD, SHERPA-ROMEO, SJFinder, Pubget, SciLit, Journal Finder, NYU Health Sciences Library, BIU Santé, Science Library Index, Ingenta Connect

Index Copernicus Value (ICV) 2018: 100.00

Pediatric Urology Case Reports journal does not charge a fee for submission, processing of manuscripts through peer-reviews, editing or publication of the articles.

Creative Commons License
Pediatric Urology Case Reports is licensed under a Creative Commons Attribution 4.0 International License.


eztekno