Incomplete duplex renal system with severe obstruction at the uretero-ureteral junction and minor obstruction at the common stem-vesical junction: Challenging diagnosis and conclusive laparoscopic treatment

Marianna Iaquinto, Roberto De Castro, Maria-Grazia Scarpa, Alessia Cerrina, Daniela Codrich, Edoardo Guida, Federica Pederiva, Maria Antonietta Lembo, Flora Maria Murru, Jurgen Schleef


Twin obstructive megaureters associated with duplex renal system is a rare malformation, particularly when a giant ureter dilation is present. We report an original case, initially misinterpreted, of a right incomplete duplex renal system with huge disproportion between the upper pole giant megaureter and the lower pole moderate megaureter, with severe obstruction at the uretero-ureteral junction and minor obstruction at the uretero-vesical junction. Uromagnetic resonance imaging allowed conclusive diagnosis and the laparoscopic approach was effective for definitive, successful treatment.


Incomplete duplex renal system, uretero-ureteral junction obstruction, giant megaureter, laparoscopic heminephrectomy

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